{
  "data": {
    "__count": 1,
    "__licence": {
      "identifier": "CC-BY-4.0",
      "link": "https://creativecommons.org/licenses/by/4.0",
      "name": "Creative Commons Attribution 4.0 International"
    },
    "results": {
      "Date": "2026-06-23 07:57:58",
      "DisorderGroup": "Disorder",
      "ORPHAcode": 171,
      "OrphanetURL": "http://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=171",
      "Preferred term": "Primary sclerosing cholangitis",
      "Prevalence": [
        {
          "PrevalenceClass": "1-9 / 1 000 000",
          "PrevalenceGeographic": "Europe",
          "PrevalenceQualification": "Value and class",
          "PrevalenceType": "Annual incidence",
          "PrevalenceValidationStatus": "Validated",
          "Source": "21351115[PMID]_[EXPERT]",
          "ValMoy": "0.77"
        },
        {
          "PrevalenceClass": "1-9 / 100 000",
          "PrevalenceGeographic": "Europe",
          "PrevalenceQualification": "Value and class",
          "PrevalenceType": "Point prevalence",
          "PrevalenceValidationStatus": "Validated",
          "Source": "ORPHANET_9489916[PMID]_18433916[PMID]_23775876[PMID]_7890895[PMID]_20683956[PMID]",
          "ValMoy": "7.84"
        },
        {
          "PrevalenceClass": "1-9 / 100 000",
          "PrevalenceGeographic": "Worldwide",
          "PrevalenceQualification": "Value and class",
          "PrevalenceType": "Point prevalence",
          "PrevalenceValidationStatus": "Validated",
          "Source": "22245904[PMID]",
          "ValMoy": "8.1"
        },
        {
          "PrevalenceClass": "1-9 / 1 000 000",
          "PrevalenceGeographic": "Worldwide",
          "PrevalenceQualification": "Value and class",
          "PrevalenceType": "Annual incidence",
          "PrevalenceValidationStatus": "Validated",
          "Source": "22245904[PMID]",
          "ValMoy": "0.65"
        },
        {
          "PrevalenceClass": "1-9 / 1 000 000",
          "PrevalenceGeographic": "United States",
          "PrevalenceQualification": "Value and class",
          "PrevalenceType": "Annual incidence",
          "PrevalenceValidationStatus": "Not yet validated",
          "Source": "14598252[PMID]_21351115[PMID]",
          "ValMoy": "0.77"
        },
        {
          "PrevalenceClass": "1-9 / 100 000",
          "PrevalenceGeographic": "United States",
          "PrevalenceQualification": "Value and class",
          "PrevalenceType": "Point prevalence",
          "PrevalenceValidationStatus": "Not yet validated",
          "Source": "14598252[PMID]_ORPHANET",
          "ValMoy": "8.81"
        },
        {
          "PrevalenceClass": "1-9 / 100 000",
          "PrevalenceGeographic": "Norway",
          "PrevalenceQualification": "Value and class",
          "PrevalenceType": "Annual incidence",
          "PrevalenceValidationStatus": "Validated",
          "Source": "9489916[PMID]",
          "ValMoy": "1.3"
        },
        {
          "PrevalenceClass": "1-9 / 100 000",
          "PrevalenceGeographic": "Norway",
          "PrevalenceQualification": "Value and class",
          "PrevalenceType": "Point prevalence",
          "PrevalenceValidationStatus": "Validated",
          "Source": "9489916[PMID]",
          "ValMoy": "8.5"
        },
        {
          "PrevalenceClass": "1-9 / 100 000",
          "PrevalenceGeographic": "Sweden",
          "PrevalenceQualification": "Value and class",
          "PrevalenceType": "Annual incidence",
          "PrevalenceValidationStatus": "Validated",
          "Source": "22098097[PMID]",
          "ValMoy": "1.22"
        },
        {
          "PrevalenceClass": "1-5 / 10 000",
          "PrevalenceGeographic": "Sweden",
          "PrevalenceQualification": "Value and class",
          "PrevalenceType": "Point prevalence",
          "PrevalenceValidationStatus": "Validated",
          "Source": "20683956[PMID]",
          "ValMoy": "16.2"
        },
        {
          "PrevalenceClass": "1-9 / 1 000 000",
          "PrevalenceGeographic": "United Kingdom",
          "PrevalenceQualification": "Value and class",
          "PrevalenceType": "Annual incidence",
          "PrevalenceValidationStatus": "Not yet validated",
          "Source": "18433916[PMID]_15188211[PMID]_ ORPHANET",
          "ValMoy": "0.66"
        },
        {
          "PrevalenceClass": "1-9 / 100 000",
          "PrevalenceGeographic": "United Kingdom",
          "PrevalenceQualification": "Value and class",
          "PrevalenceType": "Point prevalence",
          "PrevalenceValidationStatus": "Not yet validated",
          "Source": "18433916[PMID]_15188211[PMID]_ ORPHANET",
          "ValMoy": "8.28"
        },
        {
          "PrevalenceClass": "1-9 / 1 000 000",
          "PrevalenceGeographic": "Netherlands",
          "PrevalenceQualification": "Value and class",
          "PrevalenceType": "Annual incidence",
          "PrevalenceValidationStatus": "Validated",
          "Source": "23775876[PMID]",
          "ValMoy": "0.5"
        },
        {
          "PrevalenceClass": "1-9 / 100 000",
          "PrevalenceGeographic": "Netherlands",
          "PrevalenceQualification": "Value and class",
          "PrevalenceType": "Point prevalence",
          "PrevalenceValidationStatus": "Validated",
          "Source": "23775876[PMID]",
          "ValMoy": "6.0"
        },
        {
          "PrevalenceClass": "1-9 / 1 000 000",
          "PrevalenceGeographic": "Canada",
          "PrevalenceQualification": "Value and class",
          "PrevalenceType": "Annual incidence",
          "PrevalenceValidationStatus": "Validated",
          "Source": "17313496[PMID]",
          "ValMoy": "0.9"
        },
        {
          "PrevalenceClass": "<1 / 1 000 000",
          "PrevalenceGeographic": "Spain",
          "PrevalenceQualification": "Value and class",
          "PrevalenceType": "Annual incidence",
          "PrevalenceValidationStatus": "Validated",
          "Source": "7890895[PMID]",
          "ValMoy": "0.07"
        },
        {
          "PrevalenceClass": "1-9 / 1 000 000",
          "PrevalenceGeographic": "Spain",
          "PrevalenceQualification": "Value and class",
          "PrevalenceType": "Point prevalence",
          "PrevalenceValidationStatus": "Validated",
          "Source": "7890895[PMID]",
          "ValMoy": "0.22"
        },
        {
          "PrevalenceClass": "1-9 / 100 000",
          "PrevalenceGeographic": "Singapore",
          "PrevalenceQualification": "Value and class",
          "PrevalenceType": "Point prevalence",
          "PrevalenceValidationStatus": "Validated",
          "Source": "12164967[PMID]_22245904[PMID]",
          "ValMoy": "1.3"
        }
      ],
      "Typology": "Disease"
    }
  },
  "datasetCategory": {
    "lang": "en",
    "name": "Epidemiology of rare diseases"
  },
  "parameters": {
    "path": {
      "ORPHAcode": 171
    },
    "query": {}
  },
  "uri": "https://api.orphadata.com/rd-epidemiology/orphacodes/171"
}